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Vestibular Loss and Cerebellar Ataxia: A Practical Approach

Joffily, L; Simonyan, S; Giunti, P; Tarnutzer, AA; Koohi, N; Kaski, D; (2025) Vestibular Loss and Cerebellar Ataxia: A Practical Approach. Ear and Hearing 10.1097/AUD.0000000000001708. (In press). Green open access

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Abstract

Cerebellar ataxia has been the remit of neurology but increased awareness of genetic disorders affecting both cerebellar and vestibular function has led to a rise in their reported prevalence. It is not uncommon for such patients to be seen in otolaryngology clinics. This review explores the underlying etiologies of patients presenting with vestibular loss accompanied by signs of cerebellar ataxia and provides a practical approach to diagnosis. We provide a comprehensive overview of common conditions that can manifest with both vestibular dysfunction and cerebellar ataxia, acutely or chronically, including cerebellar strokes, thiamine deficiency, and neurodegenerative diseases such as spinocerebellar ataxias. The article explores key diagnostic approaches, including clinical examination, neuroimaging, and specialized vestibular testing, to aid in distinguishing these conditions. By focusing on practical aspects of diagnosis, we offer otolaryngology specialists an essential tool for more accurate identification and management of patients, aiming to improve patient care. We emphasize the importance of a systematic, multidisciplinary approach to managing complex vestibular cases.

Type: Article
Title: Vestibular Loss and Cerebellar Ataxia: A Practical Approach
Location: United States
Open access status: An open access version is available from UCL Discovery
DOI: 10.1097/AUD.0000000000001708
Publisher version: https://doi.org/10.1097/aud.0000000000001708
Language: English
Additional information: This is an open access article under the CC BY license (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
Keywords: CANVAS, Cerebellar ataxia, Differential diagnosis, Spinocerebellar ataxias, Stroke, Thiamine deficiency, Vestibular loss, Vestibulo-ocular reflex
UCL classification: UCL
UCL > Provost and Vice Provost Offices > School of Life and Medical Sciences
UCL > Provost and Vice Provost Offices > School of Life and Medical Sciences > Faculty of Brain Sciences
UCL > Provost and Vice Provost Offices > School of Life and Medical Sciences > Faculty of Brain Sciences > UCL Queen Square Institute of Neurology
UCL > Provost and Vice Provost Offices > School of Life and Medical Sciences > Faculty of Brain Sciences > UCL Queen Square Institute of Neurology > Clinical and Movement Neurosciences
URI: https://discovery.ucl.ac.uk/id/eprint/10212454
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