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Síndrome de lennox-gastaut com início na vida adulta? A respeito de um caso./ Late onset Lennox-Gastaut like syndrome: a case report

Trevisol-Bittencourt, PC; Sander, JW; (1990) Síndrome de lennox-gastaut com início na vida adulta? A respeito de um caso./ Late onset Lennox-Gastaut like syndrome: a case report. Arquivos de neuro-psiquiatria , 48 (4) 520 - 524. 10.1590/S0004-282X1990000400020. Green open access

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Abstract

The Lennox-Gastaut syndrome (LGS), although described earlier, was first accepted in 1966 as a form of severe childhood epileptic encephalopathy, characterized by refractory epileptic seizures of diverse types, typical EEG abnormalities and slow mental development. Apesar de ter sido relatada anteriormente, a sindrome de Lennox-Gastaut (SLG) só foi definitivamente aceita como entidade distinta em 1966. Desde então, o epônimo tem sido utilizado para designar encefalopatia severa da infância, caracterizada fundamentalmente por crises epilépticas refratárias de diversos tipos associadas com alterações eletrográficas típicas. Entretanto, vários autores consideram que o rótulo de SLG está abrigando quadros nosológicos distintos, que deveriam ser separados e individualizados. Ilustrando esta situação, o caso de um paciente que iniciou quadro de «SLG-like» aos 20 anos de idade é relatado. Adicionando mais confusão, alguns casos semelhantes têm sido descritos nos últimos anos sob variada nomenclatura. Desde que um dos principais critérios para o diagnóstico da SLG é a idade dependência, como deverão então ser chamados tais quadros? Revisão dos critérios empregados para o diagnóstico da SLG se faz necessária./ This condition, however, is surrounded by controversy as the clinical criteria used by various authors to define it are quite different. It is very likely that this eponym has been used to harbour distinct epileptic conditions, all of which have in common a slow spike and wave, complex in their EEG recording. Despite the fact that one of the hallmarks of LGS is an onset in early childhood, to add to the confusion, some cases of a LGS-like condition with onset in adulthood have been described. We report here one such case: a 28 year old man whose LGS-like condition started after severe head trauma at the age of 20. In addition we briefly review the difficulties in making this diagnosis, using this case to illustrate these aspects.

Type: Article
Title: Síndrome de lennox-gastaut com início na vida adulta? A respeito de um caso./ Late onset Lennox-Gastaut like syndrome: a case report
Open access status: An open access version is available from UCL Discovery
DOI: 10.1590/S0004-282X1990000400020
Publisher version: http://dx.doi.org/10.1590/S0004-282X1990000400020
Language: Portuguese
Additional information: Article in Portuguese. Original title: Sindrome de Lennox-Gastaut com inicio na vida adulta? A respeito de um caso. All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License.
UCL classification: UCL
UCL > Provost and Vice Provost Offices
UCL > Provost and Vice Provost Offices > School of Life and Medical Sciences
UCL > Provost and Vice Provost Offices > School of Life and Medical Sciences > Faculty of Brain Sciences
UCL > Provost and Vice Provost Offices > School of Life and Medical Sciences > Faculty of Brain Sciences > UCL Queen Square Institute of Neurology
UCL > Provost and Vice Provost Offices > School of Life and Medical Sciences > Faculty of Brain Sciences > UCL Queen Square Institute of Neurology > Clinical and Experimental Epilepsy
URI: https://discovery.ucl.ac.uk/id/eprint/1352232
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