eprintid: 1544974 rev_number: 25 eprint_status: archive userid: 608 dir: disk0/01/54/49/74 datestamp: 2017-03-16 16:49:49 lastmod: 2020-05-28 19:38:45 status_changed: 2017-03-16 16:49:49 type: article metadata_visibility: show creators_name: Schwaiger, JP creators_name: Loder, CD creators_name: Dobarro, D creators_name: Kaier, T creators_name: Reddecliffe, S creators_name: Schreiber, BE creators_name: Handler, C creators_name: Denton, CP creators_name: Coghlan, JG title: Optical coherence tomography evaluation of pulmonary arterial vasculopathy in Systemic Sclerosis ispublished: pub divisions: UCL divisions: A01 divisions: B02 divisions: C10 divisions: D17 divisions: G90 keywords: Interventional cardiology; Systemic sclerosis; Thrombosis note: This work is licensed under a Creative Commons Attribution 4.0 International License. The images or other third party material in this article are included in the article’s Creative Commons license, unless indicated otherwise in the credit line; if the material is not included under the Creative Commons license, users will need to obtain permission from the license holder to reproduce the material. To view a copy of this license, visit http://creativecommons.org/licenses/by/4.0/ abstract: Our current understanding of the pathophysiology of pulmonary vascular disease is incomplete, since information about alterations of the pulmonary vasculature in pulmonary arterial hypertension (PAH) is primarily provided by autopsy or tissue specimens. The aim of this study was to compare the distal pulmonary vasculature of <2 mm in diameter in Systemic Sclerosis (SSc) patients with (n = 17) and without (n = 5) associated PAH using Optical Coherence Tomography during Right Heart catheterization. SSc-PAH patients showed significant thickening of Intima Media Thickening Area compared to patients without PAH (27 +/- 5.8% vs. 21 +/- 1.4%, p = 0.024). A good haemodynamic response to previous targeted PAH treatment was associated with a significantly greater number of small pulmonary artery side branches <300 μm per cm vessel (3.8 +/- 1.1 vs. 1.8 +/- 1.1; p = 0.010) and not associated with Intima Media thickening Area (26 +/- 5.4% vs. 28 +/- 6.7%; p = 0.6). Unexpected evidence of pulmonary artery thrombus formation was found in 19% of SSc-PAH patients. This is the first in-vivo study demonstrating a direct link between a structural abnormality of pulmonary arteries and a response to targeted treatment in PAH. Intravascular imaging may identify subgroups that may benefit from anticoagulation. date: 2017-02-24 date_type: published official_url: http://dx.doi.org/10.1038/srep43304 oa_status: green full_text_type: pub pmcid: PMC5324107 language: eng primo: open primo_central: open_green article_type_text: Journal Article verified: verified_manual elements_id: 1212045 doi: 10.1038/srep43304 pii: srep43304 lyricists_name: Denton, Christopher lyricists_name: Handler, Clive lyricists_name: Schreiber, Benjamin lyricists_id: CPDEN87 lyricists_id: CHAND36 lyricists_id: BESCH99 actors_name: Denton, Christopher actors_id: CPDEN87 actors_role: owner full_text_status: public publication: Scientific Reports volume: 7 article_number: 43304 event_location: England issn: 2045-2322 citation: Schwaiger, JP; Loder, CD; Dobarro, D; Kaier, T; Reddecliffe, S; Schreiber, BE; Handler, C; ... Coghlan, JG; + view all <#> Schwaiger, JP; Loder, CD; Dobarro, D; Kaier, T; Reddecliffe, S; Schreiber, BE; Handler, C; Denton, CP; Coghlan, JG; - view fewer <#> (2017) Optical coherence tomography evaluation of pulmonary arterial vasculopathy in Systemic Sclerosis. Scientific Reports , 7 , Article 43304. 10.1038/srep43304 <https://doi.org/10.1038/srep43304>. Green open access document_url: https://discovery.ucl.ac.uk/id/eprint/1544974/1/reprint%20Schwaiger_et_al-2017-Scientific_Reports.pdf document_url: https://discovery.ucl.ac.uk/id/eprint/1544974/3/Schwaiger_Optical_coherence_tomography_Suppl.pdf