eprintid: 1418933 rev_number: 43 eprint_status: archive userid: 608 dir: disk0/01/41/89/33 datestamp: 2014-06-12 07:56:18 lastmod: 2019-10-19 08:10:01 status_changed: 2014-06-12 07:56:18 type: thesis metadata_visibility: show item_issues_count: 0 creators_name: Zhang, T title: The role of ATMIN in regulating ATM signalling ispublished: unpub divisions: A01 divisions: B02 divisions: C08 keywords: ATM, ATMIN, DNA damage abstract: Ataxia telangiectasia-mutated (ATM), the protein kinase that is mutated in patients with ataxia telangiectasia (A-T), is a central player in the cellular response to DNA damage. ATM is activated following double-strand breaks by MRE11-RAD50-NBS1 complex (MRN), which acts as an initial sensor of DSB. ATM is also activated by stimuli that change chromatin structure such as chloroquine and hypotonic shock, which depends on the ATM-interactor protein (ATMIN) as a cofactor. In this study, I show that there exists competition between ATMIN and NBS1 for ATM binding and this can regulate ATM signalling. The absence of one cofactor can lead to enhanced signalling through the alternative pathway. Furthermore, I also characterise the role of an E3 ligase that regulate the interaction between ATMIN and ATM by mediating ATMIN mono-ubiquitination. Thus ATMIN ubiquitination could be an important step in ensuring robust ATM activation after IR. In addition, I also show that ATMIN is required for ATM signalling after replication stress to protect against genomic instability in the form of anaphase bridges and aberrant chromosome segregations. ATM is activated by replication stress and is required for the formation of 53BP1-containing nuclear bodies, which protect fragile sites. ATMIN interacts with WRNIP and RAD18 in a complex that is required to activate ATM at sites of stalled replication forks. Furthermore, using a genome-wide screening approach, I identified additional factors that regulate ATM signalling after replication stress. The 8-oxo-guanosine repair pathway could represent a link between ATM signalling and genomic instability. I show that the components of base excision repair pathway are required for the activation of ATM and formation of 53BP1 nuclear bodies that protect fragile sites in the maintenance of genome stability. date: 2014-03-28 vfaculties: VFLS oa_status: green full_text_type: other thesis_class: doctoral_open language: eng thesis_view: UCL_Thesis primo: open primo_central: open_green verified: verified_manual elements_source: Manually entered elements_id: 926430 language_elements: EN lyricists_name: Zhang, Tianyi lyricists_id: TZHAN64 full_text_status: public pagerange: 1 - 215 pages: 215 institution: UCL (University College London) department: Cancer Research UK- London Research Institute thesis_type: Doctoral citation: Zhang, T; (2014) The role of ATMIN in regulating ATM signalling. Doctoral thesis , UCL (University College London). Green open access document_url: https://discovery.ucl.ac.uk/id/eprint/1418933/1/Thesis%20revised%20version%20formatted.pdf