eprintid: 10205785 rev_number: 7 eprint_status: archive userid: 699 dir: disk0/10/20/57/85 datestamp: 2025-03-10 08:26:16 lastmod: 2025-03-10 08:26:16 status_changed: 2025-03-10 08:26:16 type: article metadata_visibility: show sword_depositor: 699 creators_name: Palagyi, A creators_name: Sengupta, A creators_name: Moorthy, M creators_name: Malik, C creators_name: Barratt, J creators_name: Devuyst, O creators_name: Ulasi, II creators_name: Gale, DP creators_name: Wang, S creators_name: Angell, B creators_name: Jha, V creators_name: Jan, S title: Systematic Scoping Review of Socioeconomic Burden and Associated Psychosocial Impact in Patients With Rare Kidney Diseases and Their Caregivers ispublished: pub divisions: UCL divisions: B02 divisions: C10 divisions: D17 divisions: G93 keywords: education; lost productivity; rare kidney diseases; scoping review; socioeconomic burden note: © 2024 International Society of Nephrology. Published by Elsevier Inc. This is an open access article under the CC BYNC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/). abstract: Introduction: Rare kidney diseases constitute a significant public health challenge but have attracted limited research investment. The evidence about the socioeconomic burden of rare kidney diseases has not been systematically examined. Such evidence is critical for generating the advocacy and awareness necessary to impel scientific and policy investment in targeted care in health systems worldwide. We aimed to evaluate the socioeconomic burden borne by patients with rare kidney diseases, their families, and caregivers, and the related psychosocial impact. Methods: We undertook a systemic scoping review of the recent evidence of the socioeconomic and psychosocial burden of rare kidney diseases, to identify gaps in the understanding of this burden across contexts and factors influencing them. Three databases and the grey literature were searched for relevant studies published in the 10 years before April 30, 2023. Results: Fifty-three articles met the inclusion criteria; one-quarter of these articles included rare disease cohorts in which the kidney was the primary organ affected, and 91% of studies were conducted in high-income countries. Evidence of substantial life-long socioeconomic burden emerged across the following 4 main categories: education (n = 17 articles [32%]), work and employment (n = 40 [75%] articles), psychosocial and emotional impact (n = 17 [32%]), and out-of-pocket expenses (n = 15 [28%]). Conclusion: Significant gaps in our understanding of the socioeconomic burden remain, particularly in lower-resource health systems, among traditionally marginalized populations, and for rare diseases for which kidney is the primary affected organ. Further exploration of socioeconomic burden within these populations is vital to inform effectively targeted investment in advocacy and health care innovation for affected individuals. date: 2025-03-01 date_type: published publisher: Elsevier BV official_url: https://doi.org/10.1016/j.ekir.2024.12.005 oa_status: green full_text_type: pub language: eng primo: open primo_central: open_green verified: verified_manual elements_id: 2355482 doi: 10.1016/j.ekir.2024.12.005 lyricists_name: Gale, Daniel lyricists_id: DGALE18 actors_name: Gale, Daniel actors_id: DGALE18 actors_role: owner full_text_status: public publication: Kidney International Reports volume: 10 number: 3 pagerange: 838-854 issn: 2468-0249 citation: Palagyi, A; Sengupta, A; Moorthy, M; Malik, C; Barratt, J; Devuyst, O; Ulasi, II; ... Jan, S; + view all <#> Palagyi, A; Sengupta, A; Moorthy, M; Malik, C; Barratt, J; Devuyst, O; Ulasi, II; Gale, DP; Wang, S; Angell, B; Jha, V; Jan, S; - view fewer <#> (2025) Systematic Scoping Review of Socioeconomic Burden and Associated Psychosocial Impact in Patients With Rare Kidney Diseases and Their Caregivers. Kidney International Reports , 10 (3) pp. 838-854. 10.1016/j.ekir.2024.12.005 <https://doi.org/10.1016/j.ekir.2024.12.005>. Green open access document_url: https://discovery.ucl.ac.uk/id/eprint/10205785/1/2025%20Palagyi%20et%20al%20Scoping%20Review%20of%20Psychosocial%20impact%20of%20RKDs%20Kindey%20Int%20Rep.pdf