eprintid: 10204836 rev_number: 6 eprint_status: archive userid: 699 dir: disk0/10/20/48/36 datestamp: 2025-02-18 12:06:15 lastmod: 2025-02-18 12:06:15 status_changed: 2025-02-18 12:06:15 type: article metadata_visibility: show sword_depositor: 699 creators_name: Denton, Christopher P creators_name: Kowal-Bielecka, Otylia creators_name: Proudman, Susanna M creators_name: Olesińska, Marzena creators_name: Worm, Margitta creators_name: Del Papa, Nicoletta creators_name: Matucci-Cerinic, Marco creators_name: Radewonuk, Jana creators_name: Jochems, Jeanine creators_name: Panaite, Adrian creators_name: Shebl, Amgad creators_name: Krupa, Anna creators_name: Allanore, Yannick creators_name: Hofmann, Jutta H creators_name: Gasior, Maria J title: A Phase 2 randomised trial of safety and pharmacokinetics of IgPro20 and IgPro10 in patients with diffuse cutaneous systemic sclerosis ispublished: inpress divisions: UCL divisions: B02 divisions: C10 divisions: D17 divisions: G90 keywords: Pharmacokinetics, subcutaneous immunoglobulin, intravenous immunoglobulin, systemic sclerosis note: © The Author(s) 2025. Published by Oxford University Press on behalf of the British Society for Rheumatology. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (https://creativecommons.org/licenses/by/4.0/). abstract: OBJECTIVES: The primary objective was the safety of subcutaneous immunoglobulin, IgPro20 (Hizentra, CSL Behring) in adults with diffuse cutaneous systemic sclerosis (dcSSc). Secondary objectives included pharmacokinetics and relative bioavailability of IgPro20, and safety and pharmacokinetics of intravenous immunoglobulin, IgPro10 (Privigen, CSL Behring). METHODS: In this prospective, multicentre, randomised, open-label, crossover Phase 2 study (NCT04137224), patients (aged ≥18 years) with dcSSc were assigned to 16 weeks of IgPro20 (0.5 g/kg/week) followed by 16 weeks of IgPro10 (2 g/kg/4 weeks over 2–5 sessions), or vice-versa. Treatment-emergent adverse events (TEAEs), serious adverse events (SAEs), infusion site reactions (ISRs), clinical tests, pharmacokinetic and bioavailability were assessed. RESULTS: Twenty-seven patients were randomised from 9 October 2019–31 August 2021. In total, 22 patients (81.5%) experienced 107 TEAEs (IgPro20, 49; IgPro10, 58); most were mild/moderate. Six patients (22.2%) experienced ten SAEs (IgPro20, 6; IgPro10, 4); no treatment-related SAEs and no deaths were reported. IgPro20 ISR rate was low (2 per 100 infusions). Maximum immunoglobulin G concentration (mean [standard deviation]) was numerically lower following IgPro20 (23.7 [1.2] g/l) vs IgPro10 (46.1 [1.2] g/l), as was the geometric mean dose-normalised, baseline-corrected area under the concentration-time curve from time point 0 to tau (IgPro20, 44.8 [1.4] h*g/l; IgPro10, 60.2 [1.4] h*g/l). The bioavailability of IgPro20 relative to IgPro10 was 76.1%. CONCLUSION: This study shows that in patients with dcSSc, safety, pharmacokinetic and bioavailability profiles of IgPro20, and safety and pharmacokinetics of IgPro10, are similar to those observed in other approved indications. date: 2025-02-05 date_type: published publisher: Oxford University Press (OUP) official_url: https://doi.org/10.1093/rheumatology/keaf066 oa_status: green full_text_type: other language: eng primo: open primo_central: open_green verified: verified_manual elements_id: 2359993 doi: 10.1093/rheumatology/keaf066 lyricists_name: Denton, Christopher lyricists_id: CPDEN87 actors_name: Denton, Christopher actors_id: CPDEN87 actors_role: owner full_text_status: public publication: Rheumatology citation: Denton, Christopher P; Kowal-Bielecka, Otylia; Proudman, Susanna M; Olesińska, Marzena; Worm, Margitta; Del Papa, Nicoletta; Matucci-Cerinic, Marco; ... Gasior, Maria J; + view all <#> Denton, Christopher P; Kowal-Bielecka, Otylia; Proudman, Susanna M; Olesińska, Marzena; Worm, Margitta; Del Papa, Nicoletta; Matucci-Cerinic, Marco; Radewonuk, Jana; Jochems, Jeanine; Panaite, Adrian; Shebl, Amgad; Krupa, Anna; Allanore, Yannick; Hofmann, Jutta H; Gasior, Maria J; - view fewer <#> (2025) A Phase 2 randomised trial of safety and pharmacokinetics of IgPro20 and IgPro10 in patients with diffuse cutaneous systemic sclerosis. Rheumatology 10.1093/rheumatology/keaf066 <https://doi.org/10.1093/rheumatology%2Fkeaf066>. (In press). Green open access document_url: https://discovery.ucl.ac.uk/id/eprint/10204836/1/Denton%20et%20al_SSc%20MS_Rheumatology_Manuscript_for%20UCL%20upload.pdf