eprintid: 10198684 rev_number: 7 eprint_status: archive userid: 699 dir: disk0/10/19/86/84 datestamp: 2024-10-21 12:29:05 lastmod: 2024-10-21 12:29:05 status_changed: 2024-10-21 12:29:05 type: article metadata_visibility: show sword_depositor: 699 creators_name: Spierings, Julia creators_name: Welsing, Paco MJ creators_name: Colak, Seda creators_name: Quah, Helen creators_name: Del Galdo, Francesco creators_name: Herrick, Ariane L creators_name: Hughes, Michael creators_name: Pauling, John D creators_name: Ong, Voon H creators_name: Denton, Christopher P title: Self-reported skin severity and quality of life in systemic sclerosis: multicentre validation of PASTUL ispublished: inpress divisions: UCL divisions: B02 divisions: C10 divisions: D17 divisions: G90 keywords: patient reported outcome, quality of life, scleroderma, skin, systemic sclerosis note: This version is the author accepted manuscript. For information on re-use, please refer to the publisher’s terms and conditions. abstract: OBJECTIVES: The aim of this study was to validate the Patient self-Assessment of Skin Thickness in Upper Limb questionnaire (PASTUL) in systemic sclerosis (SSc) and assess impact of skin involvement on health-related quality of life (HRQoL). METHODS: Participants were included in four UK centres. PASTUL specifies a grading of skin at 8 sites corresponding to the modified Rodnan Skin Score (mRSS). Construct validity was assessed by comparing PASTUL scores with mRSS. HRQoL was evaluated with EQ5D5L and Leeds SSc HRQoL questionnaires. Additionally, correlation between PASTUL and Scleroderma Skin Patient reported Outcome (SSPRO) was explored. Follow-up was 12 months. RESULTS: In total, 196 participants were included, mean age was 56.4 years (SD 13.9), 80.6% female (n = 158), mean disease duration 11.9 years (SD 9.9), 110 (56.1%) had limited cutaneous (lcSSc) and 81 (41.3%) diffuse cutaneous SSc (dcSSc). PASTUL and upper limb mRSS were well correlated at baseline, 6 and 12 months (ICC = 0.67, 0.78 and 0.62, p< 0.001). Test-retest reliability was good (ICC = 0.83, p< 0.001). There was a stronger correlation between PASTUL and upper limb mRSS in dcSSc compared with lcSSc (0.69 vs 0.51, p< 0.001). In participants with early disease (< 4 years) PASTUL was moderately correlated with HRQoL (r = 0.53, p< 0.001), correlations were weaker in the whole group. Mean time to do the PASTUL self-assessment was 5.0 min (SD 3.7). CONCLUSION: PASTUL is a feasible outcome tool that adds to assessments as SSPRO. Skin thickening is correlated with HRQoL, particularly in early disease. date: 2024-10-14 date_type: published publisher: Oxford University Press (OUP) official_url: http://dx.doi.org/10.1093/rheumatology/keae561 full_text_type: other language: eng verified: verified_manual elements_id: 2327846 doi: 10.1093/rheumatology/keae561 medium: Print-Electronic pii: 7821206 lyricists_name: Denton, Christopher lyricists_name: Ong, Voon lyricists_id: CPDEN87 lyricists_id: VONGX45 actors_name: Bracey, Alan actors_id: ABBRA90 actors_role: owner full_text_status: restricted publication: Rheumatology article_number: keae561 event_location: England issn: 1462-0324 citation: Spierings, Julia; Welsing, Paco MJ; Colak, Seda; Quah, Helen; Del Galdo, Francesco; Herrick, Ariane L; Hughes, Michael; ... Denton, Christopher P; + view all <#> Spierings, Julia; Welsing, Paco MJ; Colak, Seda; Quah, Helen; Del Galdo, Francesco; Herrick, Ariane L; Hughes, Michael; Pauling, John D; Ong, Voon H; Denton, Christopher P; - view fewer <#> (2024) Self-reported skin severity and quality of life in systemic sclerosis: multicentre validation of PASTUL. Rheumatology , Article keae561. 10.1093/rheumatology/keae561 <https://doi.org/10.1093/rheumatology%2Fkeae561>. (In press). document_url: https://discovery.ucl.ac.uk/id/eprint/10198684/1/keae561.pdf