eprintid: 10196186 rev_number: 9 eprint_status: archive userid: 699 dir: disk0/10/19/61/86 datestamp: 2024-08-27 12:56:15 lastmod: 2024-08-27 12:56:15 status_changed: 2024-08-27 12:56:15 type: article metadata_visibility: show sword_depositor: 699 creators_name: Vivarelli, Marina creators_name: Barratt, Jonathan creators_name: Beck Jr, Laurence H creators_name: Fakhouri, Fadi creators_name: Gale, Daniel P creators_name: Goicoechea de Jorge, Elena creators_name: Mosca, Marta creators_name: Noris, Marina creators_name: Pickering, Matthew C creators_name: Susztak, Katalin creators_name: Thurman, Joshua M creators_name: Cheung, Michael creators_name: King, Jennifer M creators_name: Jadoul, Michel creators_name: Winkelmayer, Wolfgang C creators_name: Smith, Richard JH title: The role of complement in kidney disease: conclusions from a Kidney Disease: Improving Global Outcomes (KDIGO) Controversies Conference ispublished: pub divisions: UCL divisions: B02 divisions: C10 divisions: D17 divisions: G93 keywords: Complement inhibitor; complement-mediated injury; glomerular injury note: Copyright © 2024 Kidney Disease: Improving Global Outcomes (KDIGO). Published by Elsevier Inc. on behalf of the International Society of Nephrology. This is an open access article under the CC BY-NC-ND license (http:// creativecommons.org/licenses/by-nc-nd/4.0/). abstract: Uncontrolled complement activation can cause or contribute to glomerular injury in multiple kidney diseases. Although complement activation plays a causal role in atypical hemolytic uremic syndrome and C3 glomerulopathy, over the past decade, a rapidly accumulating body of evidence has shown a role for complement activation in multiple other kidney diseases, including diabetic nephropathy and several glomerulonephritides. The number of available complement inhibitor therapies has also increased during the same period. In 2022, Kidney Diseases: Improving Global Outcomes (KDIGO) convened a Controversies Conference, “The Role of Complement in Kidney Disease,” to address the expanding role of complement dysregulation in the pathophysiology, diagnosis, and management of various glomerular diseases, diabetic nephropathy, and other forms of hemolytic uremic syndrome. Conference participants reviewed the evidence for complement playing a primary causal or secondary role in progression for several disease states and considered how evidence of complement involvement might inform management. Participating patients with various complement-mediated diseases and caregivers described concerns related to life planning, implications surrounding genetic testing, and the need for inclusive implementation of effective novel therapies into clinical practice. The value of biomarkers in monitoring disease course and the role of the glomerular microenvironment in complement response were examined, and key gaps in knowledge and research priorities were identified. date: 2024-09 date_type: published publisher: Elsevier BV official_url: http://dx.doi.org/10.1016/j.kint.2024.05.015 oa_status: green full_text_type: pub language: eng primo: open primo_central: open_green verified: verified_manual elements_id: 2285101 doi: 10.1016/j.kint.2024.05.015 medium: Print-Electronic pii: S0085-2538(24)00389-2 lyricists_name: Gale, Daniel lyricists_id: DGALE18 actors_name: Gale, Daniel actors_id: DGALE18 actors_role: owner full_text_status: public publication: Kidney International volume: 106 number: 3 pagerange: 369-391 event_location: United States issn: 0085-2538 citation: Vivarelli, Marina; Barratt, Jonathan; Beck Jr, Laurence H; Fakhouri, Fadi; Gale, Daniel P; Goicoechea de Jorge, Elena; Mosca, Marta; ... Smith, Richard JH; + view all <#> Vivarelli, Marina; Barratt, Jonathan; Beck Jr, Laurence H; Fakhouri, Fadi; Gale, Daniel P; Goicoechea de Jorge, Elena; Mosca, Marta; Noris, Marina; Pickering, Matthew C; Susztak, Katalin; Thurman, Joshua M; Cheung, Michael; King, Jennifer M; Jadoul, Michel; Winkelmayer, Wolfgang C; Smith, Richard JH; - view fewer <#> (2024) The role of complement in kidney disease: conclusions from a Kidney Disease: Improving Global Outcomes (KDIGO) Controversies Conference. Kidney International , 106 (3) pp. 369-391. 10.1016/j.kint.2024.05.015 <https://doi.org/10.1016/j.kint.2024.05.015>. Green open access document_url: https://discovery.ucl.ac.uk/id/eprint/10196186/1/Gale_1-s2.0-S0085253824003892-main.pdf