eprintid: 10133224 rev_number: 22 eprint_status: archive userid: 608 dir: disk0/10/13/32/24 datestamp: 2021-08-19 15:09:19 lastmod: 2021-10-15 23:04:31 status_changed: 2021-08-19 15:09:19 type: article metadata_visibility: show creators_name: Rezk, T creators_name: Salota, R creators_name: Gan, JJ creators_name: Lachmann, HJ creators_name: Fontana, M creators_name: Siew, K creators_name: Martinez-Naharro, A creators_name: Guillotte, C creators_name: Bass, P creators_name: Sachchithanantham, S creators_name: Mahmood, S creators_name: Petrie, A creators_name: Whelan, CJ creators_name: Pinney, JH creators_name: Dockrell, M creators_name: Foard, D creators_name: Lane, T creators_name: Wechalekar, AD creators_name: Hawkins, PN creators_name: Walsh, SB creators_name: Gillmore, JD title: Urinary retinol binding protein predicts renal outcome in systemic immunoglobulin light-chain (AL) amyloidosis ispublished: pub divisions: UCL divisions: B02 divisions: C10 divisions: D17 divisions: G90 divisions: G93 divisions: D21 keywords: Science & Technology, Life Sciences & Biomedicine, Hematology, amyloid, myeloma, chemotherapy, renal medicine note: This is an open access article under the terms of the Creative Commons Attribution-NonCommercial-NoDerivs License, which permits use and distribution in any medium, provided the original work is properly cited, the use is non-commercial and no modifications or adaptations are made. abstract: Summary: Renal risk stratification in systemic immunoglobulin light-chain (AL) amyloidosis is according to estimated glomerular filtration rate (eGFR) and urinary protein creatinine ratio (uPCR), the latter attributed to glomerular dysfunction, with proximal tubular dysfunction (PTD) little studied. Urinary retinol binding protein 4 (uRBP), a low molecular weight tubular protein and highly sensitive marker of PTD, was prospectively measured in 285 newly diagnosed, untreated patients with systemic AL amyloidosis between August 2017 to August 2018. At diagnosis, the uRBP/creatinine ratio (uRBPCR) correlated with serum creatinine (r = 0·618, P < 0·0001), uPCR (r = 0·422, P < 0·0001) as well as both fractional excretion of phosphate and urate (r = 0·563, P < 0·0001). Log uRBPCR at diagnosis was a strong independent predictor of end-stage renal disease {hazard ratio [HR] 2·65, [95% confidence interval (CI) 1·06–6·64]; P = 0·038}, particularly in patients with an eGFR >30 ml/min/1.73 m2 [HR 4·11, (95% CI 1·45–11·65); P = 0·008] and those who failed to achieve a deep haematological response to chemotherapy within 3 months of diagnosis [HR 6·72, (95% CI 1·83–24·74); P = 0·004], and also predicted renal progression [HR 1·91, (95% CI 1·18–3·07); P = 0·008]. Elevated uRBPCR indicates PTD and predicts renal outcomes independently of eGFR, uPCR and clonal response in systemic AL amyloidosis. The role of uRBPCR as a novel prognostic biomarker merits further study, particularly in monoclonal gammopathies of renal significance. date: 2021-08-09 date_type: published publisher: WILEY official_url: https://doi.org/10.1111/bjh.17706 oa_status: green full_text_type: pub language: eng primo: open primo_central: open_green verified: verified_manual elements_id: 1882858 doi: 10.1111/bjh.17706 lyricists_name: Fontana, Marianna lyricists_name: Gillmore, Julian lyricists_name: Hawkins, Philip lyricists_name: Lachmann, Helen lyricists_name: Petrie, Aviva lyricists_name: Rezk, Tamer lyricists_name: Siew, Keith lyricists_name: Walsh, Stephen lyricists_name: Wechalekar, Ashutosh lyricists_id: MFONT56 lyricists_id: JGILL78 lyricists_id: PNHAW77 lyricists_id: HJLAC80 lyricists_id: APETR26 lyricists_id: TMIRE17 lyricists_id: KSIEW63 lyricists_id: SBWAL99 lyricists_id: AWECH53 actors_name: Flynn, Bernadette actors_id: BFFLY94 actors_role: owner full_text_status: public publication: British Journal of Haematology pages: 8 citation: Rezk, T; Salota, R; Gan, JJ; Lachmann, HJ; Fontana, M; Siew, K; Martinez-Naharro, A; ... Gillmore, JD; + view all <#> Rezk, T; Salota, R; Gan, JJ; Lachmann, HJ; Fontana, M; Siew, K; Martinez-Naharro, A; Guillotte, C; Bass, P; Sachchithanantham, S; Mahmood, S; Petrie, A; Whelan, CJ; Pinney, JH; Dockrell, M; Foard, D; Lane, T; Wechalekar, AD; Hawkins, PN; Walsh, SB; Gillmore, JD; - view fewer <#> (2021) Urinary retinol binding protein predicts renal outcome in systemic immunoglobulin light-chain (AL) amyloidosis. British Journal of Haematology 10.1111/bjh.17706 <https://doi.org/10.1111/bjh.17706>. Green open access document_url: https://discovery.ucl.ac.uk/id/eprint/10133224/1/bjh.17706.pdf