eprintid: 10055666 rev_number: 27 eprint_status: archive userid: 608 dir: disk0/10/05/56/66 datestamp: 2018-09-11 16:10:43 lastmod: 2021-09-19 22:22:57 status_changed: 2018-09-11 16:10:43 type: article metadata_visibility: show creators_name: Stichel, D creators_name: Ebrahimi, A creators_name: Reuss, D creators_name: Schrimpf, D creators_name: Ono, T creators_name: Shirahata, M creators_name: Reifenberger, G creators_name: Weller, M creators_name: Hänggi, D creators_name: Wick, W creators_name: Herold-Mende, C creators_name: Westphal, M creators_name: Brandner, S creators_name: Pfister, SM creators_name: Capper, D creators_name: Sahm, F creators_name: von Deimling, A title: Distribution of EGFR amplification, combined chromosome 7 gain and chromosome 10 loss, and TERT promoter mutation in brain tumors and their potential for the reclassification of IDHwt astrocytoma to glioblastoma ispublished: pub subjects: UCH divisions: UCL divisions: B02 divisions: C07 divisions: D07 divisions: F86 keywords: 7+/10q−, 7+/10−, Astrocytoma, Chromosome 10 loss, Chromosome 7 gain, EGFR amplification, Glioblastoma, Pleomorphic xanthoastrocytoma, TERT promoter mutation note: This version is the author accepted manuscript. For information on re-use, please refer to the publisher’s terms and conditions. abstract: EGFR amplification (EGFRamp), the combination of gain of chromosome 7 and loss of chromosome 10 (7+/10-), and TERT promoter mutation (pTERTmut) are alterations frequently observed in adult IDH-wild-type (IDHwt) glioblastoma (GBM). In the absence of endothelial proliferation and/or necrosis, these alterations currently are considered to serve as a surrogate for upgrading IDHwt diffuse or anaplastic astrocytoma to GBM. Here, we set out to determine the distribution of EGFRamp, 7+/10-, and pTERTmut by analyzing high-resolution copy-number profiles and next-generation sequencing data of primary brain tumors. In addition, we addressed the question whether combinations of partial gains on chromosome 7 and partial losses on chromosome 10 exhibited a diagnostic and prognostic value similar to that of complete 7+/10-. Several such combinations proved relevant and were combined as the 7/10 signature. Our results demonstrate that EGFRamp and the 7/10 signature are closely associated with IDHwt GBM. In contrast, pTERTmut is less specific for IDHwt GBM. We conclude that, in the absence of endothelial proliferation and/or necrosis, the detection of EGFRamp is a very strong surrogate marker for the diagnosis of GBM in IDHwt diffuse astrocytic tumors. The 7/10 signature is also a strong surrogate marker. However, care should be taken to exclude pleomorphic xanthoastrocytoma. pTERTmut is less restricted to this entity and needs companion analysis by other molecular markers to serve as a surrogate for diagnosing IDHwt GBM. A combination of any two of EGFRamp, the 7/10 signature and pTERTmut, is highly specific for IDHwt GBM and the combination of all three alterations is frequent and exclusively seen in IDHwt GBM. date: 2018-11 date_type: published official_url: https://doi.org/10.1007/s00401-018-1905-0 oa_status: green full_text_type: other language: eng primo: open primo_central: open_green article_type_text: Journal Article verified: verified_manual elements_id: 1582271 doi: 10.1007/s00401-018-1905-0 pii: 10.1007/s00401-018-1905-0 lyricists_name: Brandner, Sebastian lyricists_id: SBRAN30 actors_name: Stacey, Thomas actors_id: TSSTA20 actors_role: owner full_text_status: public publication: Acta Neuropathologica volume: 136 number: 5 pagerange: 793-803 event_location: Germany issn: 1432-0533 citation: Stichel, D; Ebrahimi, A; Reuss, D; Schrimpf, D; Ono, T; Shirahata, M; Reifenberger, G; ... von Deimling, A; + view all <#> Stichel, D; Ebrahimi, A; Reuss, D; Schrimpf, D; Ono, T; Shirahata, M; Reifenberger, G; Weller, M; Hänggi, D; Wick, W; Herold-Mende, C; Westphal, M; Brandner, S; Pfister, SM; Capper, D; Sahm, F; von Deimling, A; - view fewer <#> (2018) Distribution of EGFR amplification, combined chromosome 7 gain and chromosome 10 loss, and TERT promoter mutation in brain tumors and their potential for the reclassification of IDHwt astrocytoma to glioblastoma. Acta Neuropathologica , 136 (5) pp. 793-803. 10.1007/s00401-018-1905-0 <https://doi.org/10.1007/s00401-018-1905-0>. Green open access document_url: https://discovery.ucl.ac.uk/id/eprint/10055666/7/Brandner%20ANEU-D-18-00510_R1.pdf