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Number of items: 90.


Aguzzi, A; Klein, MA; Montrasio, F; Pekarik, V; Brandner, S; Furukawa, H; Kaser, P; (2000) Prions: Pathogenesis and reverse genetics. MOLECULAR BASIS OF DEMENTIA , 920 140 - 157.

Aguzzi, A; Raeber, AJ; Brandner, S; Frigg, R; Raeber, AJ; Hegyi, I; Rockl, C; (2000) Molecular pathology of prion diseases. J PATHOL , 190 65A - 65A.


Barrow, PA; Mallucci, G; Collinge, J; Jefferys, JGR; (2000) Rescue of a physiological phenotype in mice with ablated PrP gene but expressing a transgene cassette for PrP. J PHYSIOL-LONDON , 523 203P - 204P.

Beck, JA; Lloyd, S; Hafezparast, M; Lennon-Pierce, M; Eppig, JT; Festing, MFW; Fisher, EMC; (2000) Genealogies of mouse inbred strains. NAT GENET , 24 (1) 23 - +.

Bell, K; Cairns, NJ; Lantos, PL; Rossor, MN; (2000) Immunohistochemistry distinguishes between Pick's disease and corticobasal degeneration. J NEUROL NEUROSUR PS , 69 (6) 835 - 836.

Benninger, Y; Marino, S; Hardegger, R; Weissmann, C; Aguzzi, A; Brandner, S; (2000) Differentiation and histological analysis of embryonic stem cell-derived neural transplants in mice. BRAIN PATHOL , 10 (3) 330 - 341.

Bhatia, KP; Lee, MS; Rinne, JO; Revesz, T; Scaravilli, F; Davies, L; Marsden, CD; (2000) Corticobasal degeneration look-alikes. In: UNSPECIFIED (169 - 182). LIPPINCOTT WILLIAMS & WILKINS

Brandner, S; Klein, MA; Aguzzi, A; (2000) Mechanisms of neuroinvasion by prions: molecular principles and present status of research. SCHWEIZ MED WSCHR , 130 (12) 435 - 442.

Brandner, S; Klein, MA; Frigg, R; Pekarik, V; Parizek, P; Raeber, A; Glatzel, M; (2000) Neuroinvasion of prions: insights from mouse models. EXP PHYSIOL , 85 (6) 705 - 712.

Brandner, S; Marine, S; Kielmann, M; Hardegger, R; Fodde, R; Aguzzi, A; (2000) The role of the adenomatous polyposis coli (APC) protein in neural differentiation. BRAIN PATHOL , 10 (4) 762 - 762.

Brex, PA; Jenkins, R; Fox, NC; Crum, WR; O'Riordan, JI; Plant, GT; Miller, DH; (2000) Detection of ventricular enlargement in patients at the earliest clinical stage of MS. NEUROLOGY , 54 (8) 1689 - 1691.


Collinge, J; (2000) Human prion diseases. BRAIN PATHOL , 10 (4) 607 - 607.

Collinge, J; (2000) Prion diseases. In: Ledingham, JGG and Warrell, DA, (eds.) Concise Oxford textbook of medicine. (pp. 1307-1311). Oxford University Press: Oxford, UK.

Collinge, J; (2000) Creutzfeldt-Jakob disease and other prion diseases. In: O'Brien, JT and Ames, D and Burns, A, (eds.) Dementia. Hodder Arnold: London, UK.


D-GEN, LTD; Collinge, J; Clarke, AR; Jackson, GS; (2000) Biological materials and methods useful in the diagnosis and treatment of prion diseases. WO/2000/026238 .

D-GEN, LTD; Collinge, J; Wadsworth, JDF; Thomas, PJD; (2000) Method to type prion proteins. WO/2000/062068 .

Darmon, AJ; Jat, PS; (2000) BAP37 and Prohibitin are specifically recognized by an SV40 T antigen antibody. Mol Cell Biol Res Commun , 4 (4) pp. 219-223. 10.1006/mcbr.2001.0281.


Festing, MFW; Fisher, EMC; (2000) Mighty mice - Clarence Little's brainwave gave biomedical researchers their best friend. NATURE , 404 (6780) 815 - 815.

Fox, NC; Cousens, S; Scahill, R; Harvey, RJ; Rossor, MN; (2000) Using serial registered brain magnetic resonance imaging to measure disease progression in Alzheimer disease - Power calculations and estimates of sample size to detect treatment effects. ARCH NEUROL-CHICAGO , 57 (3) 339 - 344.

Fox, NC; Jenkins, R; Leary, SM; Stevenson, VL; Losseff, NA; Crum, WR; Harvey, RJ; (2000) Progressive cerebral atrophy in MS - A serial study using registered, volumetric MRI. NEUROLOGY , 54 (4) 807 - 812.

Fox, NC; Rossor, MN; (2000) Seeing what Alzheimer saw - with magnetic resonance microscopy. NAT MED , 6 (1) 20 - 21.

Fox, NC; Rossor, MN; (2000) Seeing what Alzheimer saw--with magnetic resonance microscopy. Nat Med , 6 (1) pp. 20-21. 10.1038/71481.


Geddes, JF; Jansen, GH; Robinson, SFD; Gomori, E; Holton, JL; Monson, JP; Besser, GM; (2000) 'Gangliocytomas' of the pituitary - A heterogeneous group of lesions with differing histogenesis. AM J SURG PATHOL , 24 (4) 607 - 613.

Ghiso, J; Vidal, R; Rostagno, A; Mead, S; Revesz, T; Plant, G; Frangione, B; (2000) A newly formed amyloidogenic fragment due to a stop codon mutation causes familial British dementia. VASCULAR FACTORS IN ALZHEIMER'S DISEASE , 903 129 - 137.

Ghiso, J; Vidal, R; Rostagno, A; Miravalle, L; Holton, JL; Mead, S; Revesz, T; (2000) Amyloidogenesis in familial British dementia is associated with a genetic defect on chromosome 13. MOLECULAR BASIS OF DEMENTIA , 920 84 - 92.

Glatzel, M; Klein, MA; Brandner, S; Aguzzi, A; (2000) Prions: from neurografts to neuroinvasion. In: ARCHIVES OF VIROLOGY. (pp. 3 - 12). SPRINGER-VERLAG WIEN

Glatzel, M; Klein, MA; Brandner, S; Aguzzi, A; (2000) Prions: from neurografts to neuroinvasion. PRION DISEASES 3 - 12.

Goold, RG; Gordon-Weeks, PR; (2000) MAP1B phosphorylation by GSK3beta is induced by NGF and is associated with neurite elongation during PC12 cell differentiation. EUROPEAN JOURNAL OF NEUROSCIENCE , 12 p. 180.


Hartmann, SL; Cash, DM; Galloway, RL; (2000) Spatially accurate 3D visualization of medical images during image-guided surgery. In: Mun, SK, (ed.) (Proceedings) Medical Imaging 2000 Conference. (pp. pp. 248-258). SPIE-INT SOC OPTICAL ENGINEERING

Hill, AF; Joiner, S; Linehan, J; Desbruslais, M; Lantos, PL; Collinge, J; (2000) Species-barrier-independent prion replication in apparently resistant species. P NATL ACAD SCI USA , 97 (18) 10248 - 10253.

Holton, JL; Lashley, T; Vidal, R; Rostagno, A; Guerin, CJ; Houlden, H; Plant, G; (2000) Familial British dementia: Immunohistochemical and immunoelectron microscopic study. BRAIN PATHOL , 10 (4) 713 - 714.

Holton, JL; Steel, T; Luxsuwong, M; Crockard, HA; Revesz, T; (2000) Skull base chordomas: correlation of tumour doubling time with age, mitosis and Ki67 proliferation index. NEUROPATH APPL NEURO , 26 (6) 497 - 503.

Houlden, H; Baker, M; McGowan, E; Lewis, P; Hutton, M; Crook, R; Wood, NW; (2000) Variant Alzheimer's disease with spastic paraparesis and cotton wool plaques is caused by PS-1 mutations that lead to exceptionally high amyloid-beta concentrations. ANN NEUROL , 48 (5) 806 - 808.

Huisman, TAGM; Brandner, S; Niggli, F; Betts, DR; Boltshauser, E; Martin, E; (2000) Malignant rhabdoid tumor of the brain: Quantitative H-1 MR-spectroscopy and cytogenetics. NEUROPEDIATRICS , 31 (3) 159 - 161.

Huisman, TAGM; Brandner, S; Niggli, F; Kacl, G; Willi, UV; Martin, E; (2000) Meningeal hemangiopericytoma in childhood. EUR RADIOL , 10 (7) 1073 - 1075.

Hunter, AJ; Hagan, JJ; Rogers, D; Nolan, P; Strivens, M; Peters, J; Brown, SDM; (2000) The discovery of novel behavioural phenotypes via a genome wide mutagenesis programme. EUR J NEUROSCI , 12 442 - 442.


Isaacs, A; Potter, A; Masih, M; Vizor, L; Oliver, P; Davies, KE; Peters, J; (2000) Evaluation of neurological mouse mutants caused by ENU mutagenesis. In: EUR J NEUROSCI. (pp. 171 - 171). BLACKWELL SCIENCE LTD

Isaacs, AM; Davies, KE; Hunter, AJ; Nolan, PM; Vizor, L; Peters, J; Gale, DG; (2000) Identification of two new Pmp22 mouse mutants using large-scale mutagenesis and a novel rapid mapping strategy. HUM MOL GENET , 9 (12) 1865 - 1871.


Jackson, GS; Collinge, J; (2000) Prion disease - the propagation of infectious protein topologies. MICROBES INFECT , 2 (12) 1445 - 1449.

Janssen, JC; Hall, M; Fox, NC; Harvey, RJ; Beck, J; Dickinson, A; Campbell, T; (2000) Alzheimer's disease due to an intronic presenilin-1 (PSEN1 intron 4) mutation - A clinicopathological study. BRAIN , 123 894 - 907.

Janssen, JC; Lantos, PL; Al-Sarraj, S; Rossor, MN; (2000) Thalamic degeneration with negative prion protein immunostaining. J NEUROL , 247 (1) 48 - 51.

Jenkins, R; Fox, NC; Rossor, AM; Harvey, RJ; Rossor, MN; (2000) Intracranial volume and Alzheimer disease - Evidence against the cerebral reserve hypothesis. ARCH NEUROL-CHICAGO , 57 (2) 220 - 224.

John, HA; Laffling, AJ; Marrs, J; Baird, A; Jat, PS; Holdstock, NB; Rossdale, PD; (2000) Establishment and characterization of equine autonomic ganglion cell lines to enable direct testing of candidate toxins involved in equine dysautonomia (grass sickness). CELL BIOL TOXICOL , 16 (1) 63 - 74.


King, A; Rossor, M; Doey, L; Collinge, J; Lantos, P; (2000) Phenotypic variations in a familiar prion disease characterised by a 144 base pair insertion in the Prion protein gene. BRAIN PATHOL , 10 (4) 669 - 669.

Krahenbuhl, S; Brandner, S; Kleinle, S; Liechti, S; Straumann, D; (2000) Mitochondrial diseases represent a risk factor for valproate-induced fulminant liver failure. LIVER , 20 (4) 346 - 348.


Lantos, PL; Reyesz, T; King, A; Cairns, NJ; Morris, HR; Janssen, J; Rossor, MN; (2000) Phenotypic variations in frontotemporal dementia caused by exon 10+16 splice site tau mutation. J NEUROPATH EXP NEUR , 59 (5) 445 - 445.

Larner, AJ; Mathias, CJ; Rossor, MN; (2000) Antonomic failure preceding dementia with Lewy bodies. J NEUROL , 247 (3) 229 - 231.

Lidington, EA; Rao, RM; Marelli-Berg, F; Jat, P; Haskard, DO; Mason, JC; (2000) Establishment and characterisation of a conditionally transformed immortalised murine cardiac endothelial cell line isolated from H2kb-tsA58 transgenic mice. CIRCULATION , 102 (18) 329 - 329.

Lloyd, SE; Onwuazor, ON; Fisher, EMC; Collinge, J; (2000) Quantitative trait locus analysis of prion disease incubation time. Presented at: Join Funders Transmissible Spongiform Encephalopathies workshop, Keele, Uk.


Mead, S; Beck, J; Dickinson, A; Fisher, EMC; Collinge, J; (2000) Examination of the human prion protein-like gene Doppel for genetic susceptibility to sporadic and variant Creutzfeldt-Jakob disease. NEUROSCI LETT , 290 (2) 117 - 120.

Mead, S; James-Galton, M; Revesz, T; Doshi, RB; Harwood, G; Pan, EL; Ghiso, J; (2000) Familial British dementia with amyloid angiopathy - Early clinical, neuropsychological and imaging findings. BRAIN , 123 975 - 991.

Moosmann, P; Brandner, S; Kleinle, S; Frauchiger, B; (2000) Hyperventilation due to mitochondrial myopathy. J ROY SOC MED , 93 (1) 25 - 26.


Nicholson, SJ; Witherden, AS; Hafezparast, M; Martin, JE; Fisher, EMC; (2000) Mice, the motor system and human motor neuron pathology. Mammalian Genome , 11 (12) pp. 1041-1052.

Nolan, PM; Peters, J; Strivens, M; Rogers, D; Hagan, J; Spurr, N; Gray, IC; (2000) A systematic, genome-wide, phenotype-driven mutagenesis programme for gene function studies in the mouse. NAT GENET , 25 (4) 440 - 443.

Nolan, PM; Peters, J; Vizor, L; Strivens, M; Washbourne, R; Hough, T; Wells, C; (2000) Implementation of a large-scale ENU mutagenesis program: towards increasing the mouse mutant resource. MAMM GENOME , 11 (7) 500 - 506.


Orth, M; Tabrizi, SJ; Schapira, AHV; (2000) Sporadic inclusion body myositis not linked to prion protein codon 129 methionine homozygosity. NEUROLOGY , 55 (8) 1235 - 1235.


Pickering-Brown, S; Baker, M; Yen, SH; Liu, WK; Hasegawa, M; Cairns, N; Lantos, PL; (2000) Pick's disease is associated with mutations in the tau gene. ANN NEUROL , 48 (6) 859 - 867.

Pickering-Brown, SM; Owen, F; Isaacs, A; Snowden, J; Varma, A; Neary, D; Furlong, R; (2000) Apolipoprotein E epsilon 4 allele has no effect on age at onset or duration of disease in cases of frontotemporal dementia with Pick- or microvacuolar-type histology. EXP NEUROL , 163 (2) 452 - 456.


Revesz, T; (2000) Axonal lesions in multiple sclerosis: an old story revisited. BRAIN , 123 203 - 204.

Revesz, T; Houlden, H; Holton, JL; Baker, M; Vowles, GH; Lashley, T; Wood, NW; (2000) Alzheimer's disease with spastic paraparesis due to deletion of exon 4 and a P436E point mutation of exon 12 of the presenilin 1 gene. BRAIN PATHOL , 10 (4) 633 - 633.

Rigby, SP; Schott, JM; Bliss, P; Higgens, CS; Kamm, MA; (2000) Dilated stomach and weak muscles. Lancet , 356 (9245) 1898-.

Rossor, MN; (2000) Dementia and driving: European national guidelines. EUROPEAN JOURNAL OF NEUROLOGY , 7 (6) p. 745. 10.1046/j.1468-1331.2000.00126.x.

Rossor, MN; EFNS Sci Panel Dementia, ; (2000) Dementia and driving: European national guidelines. EUR J NEUROL , 7 (6) 745 - 745.

Rossor, MN; Fox, NC; (2000) Mere forgetfulness or early Alzheimer's disease? ANN NEUROL , 47 (4) 419 - 420.

Rossor, MN; Revesz, T; Lantos, PL; Warrington, EK; (2000) Semantic dementia with ubiquitin-positive tau-negative inclusion bodies. BRAIN , 123 267 - 276.


Scaravilli, F; Cordery, RJ; Kretzschmar, H; Gambetti, P; Brink, B; Fritz, V; Temlett, J; (2000) Sporadic fatal insomnia: A case study. ANN NEUROL , 48 (4) 665 - 668.

Scaravilli, F; Kretschmar, H; Gambetti, P; Brink, B; An, SF; Schulz-Schaeffer, WJ; Rossor, MN; (2000) Sporadic fatal insomnia (sFI): Report of a case. J NEUROPATH EXP NEUR , 59 (5) 433 - 433.

Scaravilli, T; Pramstaller, PP; Salerno, A; Egarter-Vigl, E; Giometto, B; Vitaliani, R; An, SF; (2000) Neuronal loss in Onuf's nucleus in three patients with progressive supranuclear palsy. ANN NEUROL , 48 (1) 97 - 101.

Scaravilli, T; Pramstaller, PP; Salerno, A; Giometto, B; Revesz, T; (2000) Involvement of the Onuf nucleus in progressive supranuclear palsy. NEUROLOGY , 54 (7) A392 - A392.

Selai, CE; Trimble, MR; Rossor, MN; Harvey, RJ; (2000) The Quality of Life Assessment Schedule (QOLAS): a new method for assessing quality of life (QOL) in dementia. In: Albert, SM and Logsdon, RG, (eds.) Assessing quality of life in Alzheimer's disease. (pp. 31-48). Springer Publishing Company: New York.

Sinden, JD; Pilcher, HR; Mann, VM; Kershaw, TR; Dong, Z; Rodriguez, T; Barnetson, A; (2000) Human neural stem cells: A comparison of genetic and epigenetic approaches to long-term culturing. EUR J NEUROSCI , 12 245 - 245.

Spillantini, MG; Yoshida, H; Rizzini, C; Lantos, PL; Khan, N; Rossor, MN; Goedert, M; (2000) A novel tau mutation (N296N) in familial dementia with swollen achromatic neurons and corticobasal inclusion bodies. ANN NEUROL , 48 (6) 939 - 943.


Tabrizi, SJ; Orth, M; Wilkinson, JM; Taanman, JW; Warner, TT; Cooper, JM; Schapira, AHV; (2000) Expression of mutant alpha-synuclein causes increased susceptibility to dopamine toxicity. HUM MOL GENET , 9 (18) 2683 - 2689.

Tabrizi, SJ; Workman, J; Hart, PE; Mangiarini, L; Mahal, A; Bates, G; Cooper, JM; (2000) Mitochondrial dysfunction and free radical damage in the Huntington R6/2 transgenic mouse. ANN NEUROL , 47 (1) 80 - 86.

Tabrizi, SJ; Workman, J; Hart, PE; Mangiarini, L; Mahal, A; Bates, G; Cooper, JM; (2000) Mitochondrial dysfunction and free radical damage in the Huntington R6/2 transgenic mouse. Annals of Neurology , 47 (1) pp. 80-86. 10.1002/1531-8249(200001)47:1<80::AID-ANA13>3.3.CO;2-B.

Terry, RD; (2000) Where in the brain does Alzheimer's disease begin? Ann Neurol , 47 (4) 421-.

Thomas, NJ; Morris, CM; Scaravilli, F; Johansson, J; Rossor, M; De Lange, R; St Clair, D; (2000) Hereditary vascular dementia linked to notch 3 mutations. CADASIL in British families. Ann N Y Acad Sci , 903 pp. 293-298.


Vidal, R; Revesz, T; Rostagno, A; Kim, E; Holton, JL; Bek, T; Bojsen-Moller, M; (2000) A decamer duplication in the 3 ' region of the BRI gene originates an amyloid peptide that is associated with dementia in a Danish kindred. P NATL ACAD SCI USA , 97 (9) 4920 - 4925.

von Gunten, A; Fox, NC; Cipolotti, L; Ron, MA; (2000) A volumetric study of hippocampus and amygdala in depressed patients with subjective memory problems. J NEUROPSYCH CLIN N , 12 (4) 493 - 498.


Waldemar, G; Dubois, B; Emre, M; Scheltens, P; Tariska, P; Rossor, M; (2000) Diagnosis and management of Alzheimer's disease and other disorders associated with dementia. The role of neurologists in Europe. European Federation of Neurological Societies. Eur J Neurol , 7 (2) pp. 133-144.

Waldemar, G; Dubois, B; Emre, M; Scheltens, P; Tariska, P; Rossor, M; (2000) Diagnosis and management of Alzheimer's disease and other disorders associated with dementia. The role of neurologists in Europe. European Federation of Neurological Societies. Eur J Neurol , 7 (2) 133 - 144.

Wang, T; Sharma, SD; Fox, N; Rossor, M; Brown, MJ; Sharma, P; (2000) Description of a simple test for CADASIL disease and determination of mutation frequencies in sporadic ischaemic stroke and dementia patients. J NEUROL NEUROSUR PS , 69 (5) 652 - 654.

Warren, JD; Chatterton, B; Thompson, PD; (2000) A SPECT study of the anatomy of transient global amnesia. J Clin Neurosci , 7 (1) pp. 57-59. 10.1054/jocn.1998.0129.

Warren, JD; Kneebone, CS; (2000) Facial movement and expression disorders. Part 1. Facial weakness. Medicine Today , 1 (4) pp. 48-58.

Warren, JD; Kneebone, CS; (2000) Facial movement and expression disorders. Part 2. Excessive movement. Medicine Today , 1 (5) pp. 37-40.

Warren, JD; Smith, HB; Denson, LA; Waddy, HM; (2000) Expressive language disorder after infarction of left lentiform nucleus. J Clin Neurosci , 7 (5) pp. 456-458. 10.1054/jocn.1999.0238.

Warren, JD; Thompson, PD; Thompson, PD; (2000) Diencephalic amnesia and apraxia after left thalamic infarction. J Neurol Neurosurg Psychiatry , 68 (2) 248-.

Washbourne, R; Nolan, P; Peters, J; Vizor, L; Hewitt, M; Sellley, R; Strivens, M; (2000) Identification of novel behavioural mutations using ENU mutagenesis. EUR J NEUROSCI , 12 235 - 235.

Witherden, AS; Nicholson, SJ; Hafezparast, M; Peters, J; Ball, ST; Martin, JE; Rogers, JC; (2000) Mapping of Loa, a mouse motor deficit gene, to distal mouse chromosome 12. In: Copp, AJ and Fisher, E, (eds.) (Proceedings) Promega Young Geneticists Meeting.


Zehnder, P; Jenni, W; Brandner, S; Stäubli, M; Waespe, W; Aeschlimann, A; (2000) [Vasculitis and mononeuritis multiplex]. Praxis (Bern 1994) , 89 (18) pp. 776-784.

This list was generated on Sun May 21 05:36:59 2017 BST.